Objectives: Sudden sensorineural hearing loss (SSNHL) has several etiologies. It may be a presenting symptom of retrocochlear lesions and other CNS problems. High sensitivity and specificity rates define magnetic resonance imaging (MRI) of the brain as the gold standard for the diagnosis of retrocochlear pathologies. This study aimed to establish the incidence of CNS lesions in patients with SSNHL, and we report several unusual cases among these patients. Methods:We reviewed retrospectively the charts and MRI findings of all adult patients who presented with SSNHL between January 2012 and May 2015. We utilized gadolinium enhanced temporal bone MRI as a screening method in SSNHL patients. The study included 252 patients, 137 females and 115 males, with an average age of 51 years (range 8-82 years). Result:Of the 252 patients with SSNHL, vestibular schwannoma (VS) was found in 18 (7.1%) cases. the patients have several other CNS diseases, as Rathke’s cleft cyst, meningioma, vascular anomaly, pituitary adenoma, etc. we used glucocorticoid treatment and timely and short-term medication. Conclusion:Some vestibular schwannomas have SSNHL as initial symptoms and CNS lesions were sometimes founded incidentally in SSNHL patients. Recently, as a result of the increasing widespread use of MRI, more patients with vestibular schwannoma (VS) than expected have been detected among those with SSNHL. MRI would seem to be mandatory in all cases of SSNHL.